Résumé :
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Communication n° 267 We report an unusual patient who developed a rare form of subcutaneous cytophagic histocytic panniculitis (CHP) associated with a focal inflammatory myopathy with abundant macrophages (IMAM) 18 months after the onset of a treated dermatomyositis. At the time of this relapse, the patient had a mild hematophagocytic syndrome. Despite a meticulous search for malignancy or EBV infection, no cause was found, suggesting a continuum between 3 syndromes where T cell activation plays a more important role than previously reported: CHP, IMAM and dermatomyositis. The outcome was favorable following treatment with prednisone and azathioprine.
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