Titre : | Bezafibrate activation of PPAR drives disturbances in mitochondrial redox bioenergetics and decreases the viability of cells from patients with VLCAD deficiency |
Revue : | Biochimica et biophysica acta. Molecular basis of disease, 1867, 6 |
Auteurs : | Lund M ; Andersen KG ; Heaton R ; Hargreaves IP ; Gregersen N ; Olsen RKJ |
Type de document : | Article |
Editeur : | Netherlands, 01/06/2021 |
Langues: | Anglais |
Mots-clés: | Bezafibrate;Fatty acids oxidation deficiency;Glutathione;Inborn errors of metabolism;Mitochondria;Oxidative stress;PPAR;ROS;Thiols;VLCAD;VLCAD deficiency; |
Pubmed / DOI : | Pubmed : 33549744 / DOI : 10.1016/j.bbadis.2021.166100 |
N° Profil MNM : | 2021021 |
En ligne : | http://www.ncbi.nlm.nih.gov/pubmed/33549744 |