Titre : | Nutrition management guideline for very-long chain acyl-CoA dehydrogenase deficiency (VLCAD): An evidence- and consensus-based approach |
Revue : | Molecular genetics and metabolism |
Auteurs : | van Calcar SC ; Sowa M ; Rohr F ; Beazer J ; Setlock T ; Weihe TU ; Pendyal S ; Wallace LS ; Hansen JG ; Stembridge A ; Splett P ; Singh RH |
Type de document : | Article |
Editeur : | United States, 06/10/2020 |
Langues: | Anglais |
Mots-clés : | recommandation |
Mots-clés: | Inborn errors of metabolism;Long-chain fatty acid oxidation;Nutrition therapy/diet therapy;Practice guidelines;VLCAD deficiency;Very-long chain acyl-CoA dehydrogenase deficiency; |
Pubmed / DOI : | Pubmed : 33093005 / DOI : 10.1016/j.ymgme.2020.10.001 |
N° Profil MNM : | 2020102 |
En ligne : | http://www.ncbi.nlm.nih.gov/pubmed/33093005 |