Title: | Arginine is a disease modifier for polyQ disease models that stabilizes polyQ protein conformation |
Journal : | Brain : a journal of neurology |
Authors: | Minakawa EN ; Popiel HA ; Tada M ; Takahashi T ; Yamane H ; Saitoh Y ; Takahashi Y ; Ozawa D ; Takeda A ; Takeuchi T ; Okamoto Y ; Yamamoto K ; Suzuki M ; Fujita H ; Ito C ; Yagihara H ; Saito Y ; Watase K ; Adachi H ; Katsuno M ; Mochizuki H ; Shiraki K ; Sobue G ; Toda T ; Wada K ; Onodera O ; Nagai Y |
Material Type: | Article |
Publisher: | England, 05/2020 |
Languages: | English |
Keywords : | arginine ; CAG triplet repeats ; cell cultures ; chaperone proteins ; mouse ; spinal and bulbar muscular atrophy ; therapeutical research |
Keywords: | arginine ; chemical chaperone ; disease-modifying therapy ; polyglutamine diseases ; protein conformation |
Pubmed / DOI : | Pubmed : 32436573 / DOI : 10.1093/brain/awaa115 |
N° Profil MNM : | 2020052 |
Link for e-copy: | http://www.ncbi.nlm.nih.gov/pubmed/32436573 |