Title: | Linker proteins restore basement membrane and correct LAMA2-related muscular dystrophy in mice |
Journal : | Science translational medicine, 9, 396 |
Authors: | Reinhard JR, Author ; Lin S ; McKee KK ; Meinen S ; Crosson SC ; Sury M ; Hobbs S ; Maier G ; Yurchenco PD ; Ruegg MA |
Material Type: | Article |
Publication Date: | 2017 |
Languages: | English |
Keywords : | basal lamina ; congenital muscular dystrophy with primary merosin deficiency ; LAMA2 gene ; laminine alpha-4 ; merosin ; merosin related disease ; mouse model ; protein-protein interactions ; skeletal muscle ; transgenesis ; transgenic animals |
Pubmed / DOI : | DOI : 10.1126/scitranslmed.aal4649 / Pubmed : 28659438 |
Link for e-copy: | http://www.ncbi.nlm.nih.gov/pubmed/28659438 |