Title: | Comparison of sitting and supine forced vital capacity in collagen VI-related dystrophy and laminin Alpha2-related dystrophy |
Journal : | Pediatric pulmonology, 52, 4 |
Authors: | Meilleur KG, Author ; Linton MM ; Fontana J ; Rutkowski A ; Elliott J ; Barton M ; McGraw P ; Kokkinis A ; Donkervoort S ; Leach M ; Jain M ; Dastgir J ; Collins J ; Szczesniak R ; Yang K ; Sawnani H ; Bonnemann CG |
Material Type: | Article |
Publication Date: | 2017 |
Size: | p 524 |
Languages: | English |
Keywords : | collagen VI related disease ; congenital muscular dystrophy with primary merosin deficiency ; guidelines ; lying position ; merosin related disease ; respiratory failure ; retrospective studies ; sitting position ; sleep disorders ; vital capacity |
Keywords: | congenital muscular dystrophy;dynamic spirometry;neuromuscular disorders;pulmonary function testing;vital capacity; |
Pubmed / DOI : | DOI : 10.1002/ppul.23622 / Pubmed : 28085238 |
Link for e-copy: | http://www.ncbi.nlm.nih.gov/pubmed/28085238 |