Title: | Developmental Alterations in Heart Biomechanics and Skeletal Muscle Function in Desmin Mutants Suggest an Early Pathological Root for Desminopathies. |
Journal : | Cell reports, 11, 10 |
Authors: | Ramspacher C ; Steed E ; Boselli F ; Ferreira R ; Faggianelli N ; Roth S ; Spiegelhalter C ; Messaddeq N ; Trinh L ; Liebling M ; Chacko N ; Tessadori F ; Bakkers J ; Laporte J ; Hnia K ; Vermot J |
Material Type: | Article |
Publication Date: | 16/06/2015 |
Size: | p. 1564-76 |
Languages: | English |
Keywords : | cardiac features ; desminopathy ; intracellular calcium ; muscle contraction ; muscle fibers ; sarcoplasmic reticulum ; tubular aggregates |
Pubmed / DOI : | DOI : 10.1016/j.celrep.2015.05.010 / Pubmed : 26051936 |
Link for e-copy: | http://www.ncbi.nlm.nih.gov/pubmed/26051936 |