Title: | Sirtuin inhibition protects from the polyalanine muscular dystrophy protein PABPN1 |
Journal : | Human molecular genetics, 17, 14 |
Authors: | Catoire H ; Pasco MY ; Abu-Baker A ; Holbert S ; Tourette C ; Brais B ; Rouleau GA ; Parker JA ; Néri C |
Material Type: | Article |
Publication Date: | 2008 |
Size: | p. 2108-2117 |
Languages: | English |
Keywords : | Caenorhabditis elegans ; cell cultures ; cytotoxicity ; genetic mutations ; histones ; molecular biology ; muscle fiber degeneration ; oculopharyngeal muscular dystrophy ; PABPN1 protein ; skeletal muscle ; transcription factors |
Abstract: |
Accès au résumé PubMed / to PubMed abstract |
Lien associé : | http://www.ncbi.nlm.nih.gov/pubmed/18397876?ordinalpos=1&itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum |