Title: | Pharmacological activation of PPAR{beta}/{delta} stimulates utrophin A expression in skeletal muscle fibers and restores sarcolemmal integrity in mature mdx mice |
Journal : | Human molecular genetics, 18, 23 |
Authors: | Miura P ; Chakkalakal JV ; Boudreault L ; Bélanger G ; Hébert RL ; Renaud JM ; Jasmin BJ |
Material Type: | Article |
Publication Date: | 2009 |
Size: | p. 4640-4649 |
Languages: | English |
Keywords : | Duchenne muscular dystrophy ; dystrophin ; eccentric contractions ; gene expression ; immunofluorescence ; immunoglobulin M ; mdx mouse ; molecular biology ; muscle fibers ; myosin heavy chain ; peroxisome proliferator activated receptors ; sarcolemma ; spinal cord injury ; UTRN gene ; utrophin |
Abstract: |
Accès au résumé PubMed / to PubMed abstract |
Lien associé : | http://www.ncbi.nlm.nih.gov/pubmed/19744959?itool=EntrezSystem2.PEntrez.Pubmed.Pubmed_ResultsPanel.Pubmed_RVDocSum&ordinalpos=1 |
Pubmed / DOI : | DOI : 10.1093/hmg/ddp431 |