Mots-clés
 > MYOBASE > BIOLOGIE > biologie par discipline > biologie cellulaire
biologie cellulaireSynonyme(s)cellular biology ;cytologie ;cytology ;cell biology in situ PCR |
Mettre toutes les notices dans le panier Faire une suggestion Ajouter un critère de rechercheEtendre la recherche sur niveau(x) vers le bas
HDAC6 inhibitors: Translating genetic and molecular insights into a therapy for axonal CMT
Rossaert E, van den Bosch L
Brain research, 2020
Generation of two iPSC lines (FAMRCi006-A and FAMRCi006-B) from patient with dilated cardiomyopathy and Emery-Dreifuss muscular dystrophy associated with genetic variant LMNAp.Arg527Pro
Perepelina K, Klauzen P, Khudiakov A, et al.
Stem cell research, 2020, 43
Ubiquitin ligase LRSAM1 suppresses neurodegenerative diseases linked aberrant proteins induced cell death
Mishra R, Amanullah A, Upadhyay A, et al.
The International Journal of Biochemistry & Cell Biology, 2020, 120
Self-Organizing 3D Human Trunk Neuromuscular Organoids
Faustino Martins JM, Fischer C, Urzi A, et al.
Cell stem cell, 2020, 26, 2
AMPK Complex Activation Promotes Sarcolemmal Repair in Dysferlinopathy
Ono H, Suzuki N, Kanno SI, et al.
Molecular therapy : the journal of the American Society of Gene Therapy, 2020
Inhibition of cyclooxygenase-1 by nonsteroidal anti-inflammatory drugs demethylates MeR2 enhancer and promotes Mbnl1 transcription in myogenic cells
Huang K, Masuda A, Chen G, et al.
Scientific Reports, 2020, 10, 1
Structure-Specific Cleavage of an RNA Repeat Expansion with a Dimeric Small Molecule Is Advantageous over Sequence-Specific Recognition by an Oligonucleotide
Benhamou RI, Angelbello AJ, Andrews RJ, et al.
ACS chemical biology, 2020
Novel HDAC6 Inhibitors Increase Tubulin Acetylation and Rescue Axonal Transport of Mitochondria in a Model of Charcot-Marie-Tooth Type 2F
Adalbert R, Kaieda A, Antoniou C, et al.
ACS chemical neuroscience, 2020
Mitochondrial function in skeletal myofibers is controlled by a TRF2-SIRT3 axis over lifetime
Robin JD, Jacome Burbano MS, Peng H, et al.
Aging cell, 2020
ZPR1 prevents R-loop accumulation, upregulates SMN2 expression and rescues spinal muscular atrophy
Kannan A, Jiang X, He L, et al.
Brain : a journal of neurology, 2020, 143, 1, p 69
Intravenous immunoglobulin mediates anti-inflammatory effects in peripheral blood mononuclear cells by inducing autophagy
Das M, Karnam A, Stephen-Victor E, et al.
Cell death & disease, 2020, 11, 1, p 50
AdipoRon, a new therapeutic prospect for Duchenne muscular dystrophy
Abou-Samra M, Selvais CM, Boursereau R, et al.
Journal of cachexia, sarcopenia and muscle, 2020
On-chip 3D neuromuscular model for drug screening and precision medicine in neuromuscular disease
Osaki T, Uzel SGM, Kamm RD
Nature Protocols, 2020
Physical and Functional Cross Talk Between Endo-Sarcoplasmic Reticulum and Mitochondria in Skeletal Muscle
Boncompagni S, Pozzer D, Viscomi C, et al.
Antioxidants & redox signaling, 2019
Sporadic Inclusion Body Myositis and Other Rimmed Vacuolar Myopathies
Weihl CC
Continuum (Minneapolis, Minn.), 2019, 25, 6, p 1586
Cored in the act: the use of models to understand core myopathies
Fusto A, Moyle LA, Gilbert PM, et al.
Disease models & mechanisms, 2019, 12, 12
DeepNEU: Artificially Induced Stem Cell (aiPSC) and Differentiated Skeletal Muscle Cell (aiSkMC) Simulations of Infantile Onset POMPE Disease (IOPD) for Potential Biomarker Identification and Drug Discovery
Esmail S, Danter WR
Frontiers in cell and developmental biology, 2019, 7, p 325
Defects in G-Actin Incorporation into Filaments in Myoblasts Derived from Dysferlinopathy Patients Are Restored by Dysferlin C2 Domains
Baez-Matus X, Figueroa-Cares C, González-Jamett AM, et al.
International Journal of molecular sciences, 2019, 21, 1
Mutant lamins cause nuclear envelope rupture and DNA damage in skeletal muscle cells
Earle AJ, Kirby TJ, Fedorchak GR, et al.
Nature materials, 2019
Antisense-Mediated Skipping of Dysferlin Exons in Control and Dysferlinopathy Patient-Derived Cells
Verwey N, Gazzoli I, Krause S, et al.
Nucleic acid therapeutics, 2019
Identification of the hyaluronic acid pathway as a therapeutic target for facioscapulohumeral muscular dystrophy
DeSimone AM, Leszyk J, Wagner K, et al.
Science advances, 2019, 5, 12
Targeting the programmed axon degeneration pathway as a potential therapeutic for Charcot-Marie-Tooth disease
Moss KR, Höke A
Brain research, 2019
Force Generation by Myosin Motors: A Structural Perspective
Robert-Paganin J, Pylypenko O, Kikuti C, et al.
Chemical reviews, 2019
Muscular, Ocular and Brain Involvement Associated with a De Novo 11q13.2q14.1 Duplication: Contribution to the Differential Diagnosis of Muscle-Eye-Brain Congenital Muscular Dystrophy
Villar-Quiles RN, De la Banda MGG, Barois A, et al.
Journal of Neuromuscular Diseases, 2019
