Title: | Practical Recommendations for Diagnosis and Management of Respiratory Muscle Weakness in Late-Onset Pompe Disease |
Journal : | International Journal of molecular sciences, 17, 10 |
Authors: | Boentert M, Author ; Prigent H ; Vardi K ; Jones HN ; Mellies U ; Simonds AK ; Wenninger S ; Barrot Cortes E ; Confalonieri M |
Material Type: | Article |
Publication Date: | 2016 |
Languages: | English |
Keywords : | assisted cough ; assisted ventilation ; guidelines ; inspiratory capacity ; late-onset Pompe disease ; lungs ; muscle weakness ; respiratory failure ; respiratory management ; respiratory muscles ; vital capacity |
Keywords: | Pompe disease;cough assistance;mechanical ventilation;neuromuscular disorders;respiratory muscle weakness; |
Pubmed / DOI : | DOI : 10.3390/ijms17101735 / Pubmed : 27763517 |
Link for e-copy: | http://www.ncbi.nlm.nih.gov/pubmed/27763517 |
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