Title: | Immortalized myogenic cells from congenital muscular dystrophy type1A patients recapitulate aberrant caspase activation in pathogenesis : a new tool for MDC1A research |
Journal : | Skeletal Muscle, 3, 1, 28 |
Authors: | Yoon S ; Stadler G ; Beermann ML ; Schmidt EV ; Windelborn JA ; Schneiderat P ; Wright WE ; Miller JB |
Material Type: | Article |
Publication Date: | 2013 |
Size: | 7 p. |
Languages: | English |
Keywords : | caspases ; congenital muscular dystrophy with primary merosin deficiency ; LAMA2 gene ; merosin ; mouse model ; myoblast ; myotube ; telomerase |
Pubmed / DOI : | DOI : 10.1186/2044-5040-3-28 / Pubmed : 24314268 |