Title: | Epsilon-sarcoglycan compensates for lack of alpha-sarcoglycan in a mouse model of limb-girdle muscular dystrophy |
Journal : | Human molecular genetics, 14, 6 |
Authors: | Imamura M ; Mochizuki Y ; Engvall E ; Takeda S |
Material Type: | Article |
Publication Date: | 2005 |
Size: | p. 775-783 |
Languages: | English |
Keywords : | alpha-sarcoglycan ; alpha-sarcoglycan-related limb-girdle muscular dystrophy R3 ; autosomal recessive inheritance ; dystrophin ; dystrophin complex ; epsilon-sarcoglycan ; genetic mutations ; immunohistochemistry ; molecular biology ; mouse ; muscle injuries ; sarcolemma ; SGCA gene ; skeletal muscle |
Abstract: |
Accès au résumé PubMed / to PubMed abstract |
Lien associé : | http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=pubmed&dopt=Abstract&list_uids=15689353 |